TY - JOUR AU - González García, Pilar AU - Barriocanal Casado, Eliana AU - Díaz Casado, María Elena AU - López Herrador, Sergio AU - Hidalgo Gutiérrez, Agustín AU - López García, Luis Carlos PY - 2021 UR - http://hdl.handle.net/10481/71722 AB - Coenzyme Q (CoQ) is a vital lipophilic molecule that is endogenously synthesized in the mitochondria of each cell. The CoQ biosynthetic pathway is complex and not completely characterized, and it involves at least thirteen catalytic and regulatory... LA - eng PB - MDPI KW - Mitochondria KW - Mitochondrial disease KW - Oxidative stress KW - Pathomechanisms KW - Preclinical models KW - Sulfide metabolism KW - Therapy TI - Animal Models of Coenzyme Q Deficiency: Mechanistic and Translational Learnings DO - 10.3390/antiox10111687 ER -