Left superior vena cava draining into the left atrium: Clinical entities, diagnosis and surgical treatment Aguilar, Juan Miguel Rodríguez Serrano, Fernando Ferreiro-Marzal, Andrea Esteban-Molina, María Gabucio, Antonio García, Enrique Boni, Lorenzo Garrido, José Manuel Congenital abnormality Persistent left superior vena cava Heterotaxy syndrome Unroofed coronary sinus syndrome Surgical techniques There are two different clinical entities in which a persistent left superior vena cava (LSVC) can drain into the left atrium (LA) in the absence of coronary sinus: heterotaxy syndrome and unroofed coronary sinus syndrome (UCSS). In these cases, biventricular repair can be done by intracardiac rerouting or by disconnection-reconnection to the right atrium (RA) or to the right superior vena cava (RSVC) using extracardiac procedures. In the period from 1998 to 2016, 10 patients with LSVC draining into the LA underwent 11 surgeries for biventricular repair. The present study focuses on heterotaxy syndrome and unroofed coronary sinus syndrome (UCSS), associated cardiomyopathies, the state of the art in their surgical treatment and our results in our sample. Our experience highlights that accurate diagnosis and appropriate selection of surgical technique, considering different characteristics, such as patient anatomy, age, associated cardiomyopathies, etc., are important for patient outcome. 2024-02-09T18:50:07Z 2024-02-09T18:50:07Z 2019 info:eu-repo/semantics/article https://hdl.handle.net/10481/88923 10.1016/j.acvd.2018.05.007 eng info:eu-repo/semantics/embargoedAccess